The Malachite Wen-Myeloid Sarcoma- Crimson Publishers
Contingent
to World Health Organization (WHO) classification, myeloid sarcoma is
denominated as a tumefaction comprised of myeloblasts amalgamated at an
anatomical site divergent from the bone marrow which engenders distortion of
normal tissue architecture. Generally, myeloid sarcoma is contemplated to be
equivalent to and concurrent with acute myeloid leukaemia (AML), although
lesions may occur in isolation. Additionally designated as granulocytic
sarcoma, chloroma or extramedullary myeloid tumour, myeloid sarcoma
categorically represents as a distinct tumefaction associated with
architectural effacement of circumscribing soft tissue. Myeloid sarcoma may
emerge as a de novo lesion or manifest as therapy related myeloid neoplasm or
as disease progression within myeloproliferative neoplasm (MPN),
myelodysplastic syndrome (MDS) or myelodysplastic / myeloproliferative neoplasm
(MDS / MPN). In contrast, leukaemia cutis (LC) is a nonspecific terminology
adopted to describe cutaneous infiltration of neoplastic leukocytes which
configure as mature or immature myeloid or lymphoid cellular components.
Nevertheless, as per WHO classification criterion, leukaemia cutis remains
nonequivalent to myeloid sarcoma [1,2]. Leukaemia cutis may emerge in subjects
delineating non acute myeloid leukaemia (non-AML), Myeloproliferative Neoplasm
(MPN), Myelodysplastic Syndrome (MDS) or Myelodysplastic/ Myeloproliferative
neoplasm (MDS / MPN) as Chronic Myelomonocytic Leukemia (CMML).
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